A Case of Miyazaki Syndrome Caused by Arachnoid Cyst-Peritoneal Shunt
A Case of Miyazaki Syndrome Caused by Arachnoid Cyst-Peritoneal Shunt
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蛛网膜囊肿-腹膜分流术致宫崎综合征一例
DOI：
10.1016/j.wneu.2020.10.094
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发表时间：
2021
影响因子：
2
通讯作者：
Suzuki Hidenori
中科院分区：
文献类型：
--
作者：
Ichikawa Tomonori;Yasuda Ryuta;Maeda Masayuki;Matsuyama Hirofumi;Matsuura Keita;Asada Reona;Shiba Masato;Suzuki Hidenori
宫崎综合征是过度分流相关性脊髓病，是脑室腹腔分流术的一种罕见并发症。我们提出的第一例宫崎综合征引起的囊腹腔（CP）分流蛛网膜囊肿（AC）在此report.Case Description我们报告的情况下，一个42岁的男子12年进行性痉挛性截瘫，谁接受CP分流AC在15岁。虽然很少有研究结果表明过度分流的症状和头部计算机断层扫描，对比增强磁共振成像显示充血的颈脊髓硬膜外静脉丛压迫脊髓。用压力可调节阀置换分流阀。术后，颈髓压迫扩大脊髓硬膜外静脉丛完全改善，但可能是由于延误诊断和治疗，病人的症状只有部分improved.ConclusionsWhen患者的任何一种分流手术的历史发展脊髓病，宫崎综合征应被怀疑，早期诊断，颈部和/或对比增强磁共振成像应进行。
BackgroundMiyazaki syndrome is overshunting-associated myelopathy, which is a rare complication of ventriculoperitoneal shunt. We present the first case of Miyazaki syndrome caused by cystoperitoneal (CP) shunt for an arachnoid cyst (AC) in this report.Case DescriptionWe report a case of a 42-year-old man with 12-year progressive spastic paraplegia, who underwent CP shunt for an AC at the age of 15 years. Although few findings suggested overshunting on symptoms and head computed tomography, contrast-enhanced magnetic resonance imaging revealed the engorgement of the cervical spinal epidural venous plexus compressing the spinal cord. Shunt valve replacement with a pressure-adjustable valve was performed. Postoperatively, the cervical cord compression by the enlarged spinal epidural venous plexus was completely improved, but, possibly due to delayed diagnosis and treatment, the patient's symptoms only partially improved.ConclusionsWhen patients with a history of any kind of shunt surgery develop myelopathy, Miyazaki syndrome should be suspected and, for early diagnosis, cervical and/or contrast-enhanced magnetic resonance imaging should be performed.