[Pseudo-tumorous panniculitis of the mesentery. An unusual initial stage of acute lupus erythematosus in a 10-year-old girl].

[Pseudo-tumorous panniculitis of the mesentery. An unusual initial stage of acute lupus erythematosus in a 10-year-old girl].
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[肠系膜假瘤性脂膜炎。

DOI:
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发表时间:
1982
期刊:
La semaine des hôpitaux : organe fondé par l'Association d'enseignement médical des hôpitaux de Paris
影响因子:
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通讯作者:
G. Lebreuil
G. Lebreuil
中科院分区:
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文献类型:
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作者:
A. Dor;J. L. Kohler;P. Aubrespy;C. Scheiner;M. Pizzi;G. Lebreuil

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泛性狼疮通常累及皮下和深部真皮(伊冈氏深部狼疮)。在我们的病例中,系统性红斑狼疮之前是腹内泛膜炎,作为一个巨大的肿瘤发生。组织学检查显示常见的泛膜炎,但也有严重的纤维蛋白样坏死病变,这应该引起我们的注意。狼疮必须包括在腹内睫状体炎的病因。
Lupus panniculitis usually affects the hypodermis and the dermis profundus (Irgang's lupus profundus). In our case, the systemic lupus erythematosus was preceded by an intraabdominal panniculitis, occurring as a voluminous tumor. Histological examination showed the usual picture of panniculitis, but there were also severe fibrinoid necrotic lesions, which should have alerted us. Lupus must be included among the etiologies of intraabdominal panniculitis.