SARCOMAS RELATED TO THE HEART AND VASCULATURE
SARCOMAS RELATED TO THE HEART AND VASCULATURE
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DOI：
10.1002/ssu.2980100511
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发表时间：
1994-09-01
期刊：
影响因子：
--
通讯作者：
RAAF, JH
中科院分区：
文献类型：
--
作者：
RAAF, HN;RAAF, JH
软组织肉瘤是心脏、心包和大血管最常见的恶性肿瘤。 它的表现是罕见的，非特异性的，微妙的。 例如，从这些肿瘤到肺部或外周动脉的栓子可能与血栓性栓塞疾病相似。 新的非侵入性技术，如超声心动图和磁共振成像（MRI）辅助诊断和术前评估。 血管肉瘤，最常见的心脏肉瘤，是积极的，通常发生在右心房。 心脏卡波济氏肉瘤见于艾滋病患者和免疫抑制的器官移植受者。 大多数原发于主动脉和肺动脉（弹性动脉）的肉瘤显示出最小的分化，并被归类为“内膜肉瘤”，而平滑肌肉瘤主要发生在肌性动脉和大静脉。 在可行的情况下，手术切除任何血管肉瘤在技术上具有挑战性，但可能导致治愈或缓解。 辅助化疗和放疗也可以缓解症状，延长生存期。 (C)1994 Wiley-Liss，Inc.
Soft tissue sarcoma is the most common malignant neoplasm of the heart, pericardium, and great vessels. Its presentation is infrequent, nonspecific, and subtle. For example, emboli from these tumors to the lungs or peripheral arteries may mimic thrombotic embolic disease. New noninvasive techniques such as echocardiography and magnetic resonance imaging (MRI) aid in diagnosis and preoperative assessment. Angiosarcoma, the most common cardiac sarcoma, is aggressive and usually arises in the right atrium. Kaposi's sarcoma of the heart has been found in patients with AIDS and in immunosuppressed organ transplant recipients. Most primary sarcomas of the aorta and pulmonary artery (the elastic arteries) show minimal differentiation and are classified as ''intimal sarcomas,'' whereas leiomyosarcomas predominate in the muscular arteries and great veins. Surgical resection of any sarcoma of the vasculature, when feasible, is technically challenging but may result in cure or palliation. Adjuvant chemotherapy and radiation therapy can also relieve symptoms and prolong survival. (C) 1994 Wiley-Liss, Inc.