Rasmussen encephalitis with active inflammation and delayed seizures onset
Rasmussen encephalitis with active inflammation and delayed seizures onset
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DOI：
10.1212/01.wnl.0000115393.67403.53
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发表时间：
2004-03-23
期刊：
影响因子：
9.9
通讯作者：
Steiner, I
中科院分区：
文献类型：
--
作者：
Korn-Lubetzki, I;Bien, CG;Steiner, I
重症局灶性癫痫被认为是拉斯穆森脑炎(RE)的临床特征。作者报告两名儿童进行性偏瘫，对侧大脑半球萎缩，并具有RE的病理特征。在组织学诊断和几个月的时间里，两名患者都没有癫痫发作。该报告扩大了RE的临床范围，并表明癫痫发作不是该疾病的强制性表现症状。
Severe focal epilepsy is regarded as a clinical hallmark of Rasmussen encephalitis (RE). The authors report two children with progressive hemiparesis, contralateral hemispheric atrophy, and pathologic features characteristic for RE. At histologic diagnosis and over several months, neither patient experienced seizures. The report enlarges the clinical spectrum of RE and suggests that seizures are not an obligatory presenting symptom of the disorder.