THE MORNING GLORY SYNDROME - A MESODERMAL DEFECT
THE MORNING GLORY SYNDROME - A MESODERMAL DEFECT
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DOI：
10.1159/000309330
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发表时间：
1983-01-01
期刊：
影响因子：
2.6
通讯作者：
MCCREATH, GT
中科院分区：
文献类型：
--
作者：
DEMPSTER, AG;LEE, WR;MCCREATH, GT
临床，超声，CAT扫描和病理结果的情况下，一个罕见的单侧畸形涉及视盘的类型描述为“牵牛花综合征”。该畸形与视乳头周围巩膜缺损、筛板缺失和视神经轴向后移形成的凹陷有关。有一个相关的继发性渗出性视网膜脱离与视网膜萎缩和神经胶质增生，视网膜色素上皮细胞显示乳头周围增生。其他功能包括：（a）球后隐窝内的视网膜中明显的劈裂，（B）神经周围脑膜缺失，其被纤维脂肪组织和平滑肌束替代，（c）周围视神经萎缩和（d）视网膜中央动脉周围的血管丛。
The clinical, ultrasonographic, CAT scan and pathologic findings are described in a case of a rare unilateral malformation involving the optic disc of the type described as the ‘morning glory syndrome’. The malformation was associated with a peripapillary scleral defect, absence of the lamina cribrosa and a recess formed by an axial retrodisplacement of the optic nerve. There was an associated secondary exudative retinal detachment with retinal atrophy and gliosis; the retinal pigment epithelium showed peripapillary proliferation. Additional features included: (a) an apparent schisis in the retina within the retrobulbar recess, (b) an absence of the perineural meninges which were replaced by fibroadipose tissue and bundles of smooth muscle, (c) peripheral optic nerve atrophy and (d) a vascular plexus surrounding the central retinal artery.