Prune belly syndrome and fetal ascites.
Prune belly syndrome and fetal ascites.
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梅腹综合症和胎儿腹水。
DOI：
10.1002/tera.1420190115
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发表时间：
1979
期刊：
影响因子：
--
通讯作者：
B. J. Monie
中科院分区：
文献类型：
--
作者：
I. W. Monie;B. J. Monie
本文报告一例22周男性胎儿的梅花腹综合征。该综合征的所有特征都存在：腹肌缺失；膀胱、输尿管和肾盆扩张；以及睾丸下垂。此外，还有明显的腹水。腹直肌完全缺失，其他腹肌仅中央性缺失。在正常肌肉和缺失肌肉之间，肌纤维稀疏、肥大、经常断裂，且大多在肌小管期。前列腺是薄壁的，它的尿路大大扩张。睾丸靠近相应的输尿管，每个输精管只有部分存在。目前认为，前列腺发育不全和胎儿腹水是PBS发生的关键因素。
A case of prune belly syndrome (PBS) in a 22 week male fetus is described. All the features characteristic of the syndrome were present: absence of abdominal muscle; dilatation of the bladder, ureters, and renal pelves; and undescended testes. In addition, there was marked ascites. The rectus abdominis muscles were entirely absent whereas other abdominal muscles were only absent centrally. Between regions of normal and absent musculature muscle fibers were sparse, enlarged, frequently disrupted, and mostly in the myotubule stage. The prostate was thin-walled and its urethra greatly expanded. The testes lay close to the corresponding ureters and each ductus deferens was only partially present. It is considered that prostatic dysgenesis and fetal ascites are key factors in the causation of PBS.