Partial Anomalous Pulmonary Venous Connections
Partial Anomalous Pulmonary Venous Connections
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部分异常肺静脉连接
DOI：
10.1177/2150135112460250
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发表时间：
2013
影响因子：
0.9
通讯作者：
I. Fragata
中科院分区：
文献类型：
--
作者：
J. Fragata;M. Magalhães;L. Baquero;C. Trigo;F. Pinto;I. Fragata
部分肺静脉异位引流(PAPVCs)是一组异质性的先天性心脏病变，其中至少有一条肺静脉会引流到全身静脉系统。结果是可变的从左到右的血流动力学分流，更罕见的是肺动脉高压。PAPVC通常与其他先天性心脏畸形一起发生。手术矫正通常是可取的，而且通常是直接和简单的实现。历史上，一些修复包括切开上腔静脉与右心房的交界处，这可能会导致晚期心律失常。典狱术避免了房腔交界处的切开。患有弯曲症的新生儿和婴儿是PAPVC患者中最具挑战性的亚群。
Partial anomalous pulmonary venous connections (PAPVCs) are a heterogeneous group of congenital heart lesions in which at least one pulmonary vein will drain into the systemic venous system. The consequences are a variable left-to-right hemodynamic shunt and more rarely pulmonary artery hypertension. Often, PAPVC occurs in association with other congenital cardiac malformations. Surgical correction is most often advisable and is generally straightforward and simple to achieve. Historically, some repairs have included incision across the junction of the superior vena cava with the right atrium, which can lead to late arrhythmias. The Warden technique avoids incision across the atriocaval junction. Neonates and infants with Scimitar syndrome represent the most challenging subset of patients with PAPVC.