Anaesthetic Management in a Child with Goldenhar Syndrome.
Anaesthetic Management in a Child with Goldenhar Syndrome.
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Goldenhar 综合征儿童的麻醉管理。
DOI：
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发表时间：
2017
期刊：
影响因子：
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通讯作者：
S. Chughtai
中科院分区：
文献类型：
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作者：
W. Khan;B. Salim;A. Khan;S. Chughtai
Goldenhar综合征是一种涉及面部畸形的先天性疾病。它通常只影响一侧面部，并对气道管理构成重大挑战。我们在此报告一个8岁男孩，已知的情况下，戈登哈尔综合征，谁提出了我们的放射科套房的磁共振成像（MRI）的大脑，其次是计算机断层扫描（CT）扫描的大脑。该男孩具有Goldenhar综合征的各种特征，例如腭裂、右眼和右耳缺失、右下颌发育不全、小颌畸形和耳前突。他的发展里程碑被推迟了。气道评估显示Mallampati II级，头部和颈部活动受限，这表明可能存在喉镜检查和插管困难。他没有脊椎异常或心脏病。困难的气道仍然是麻醉相关的发病率和死亡率的主要原因，保持自主呼吸仍然是其管理的重要技术。缺乏麻醉相关的并发症与声门上装置鼓励我们提出的优势，利用喉罩气道（LMA）麻醉下成功管理预测困难的气道。
Goldenhar syndrome is a congenital disorder involving deformities of the face. It usually affects one side of the face only and poses significant challenges in the airway management. We herein, report an 8-year boy, known case of Goldenhar syndrome, who presented to our radiology suite for a magnetic resonance imaging (MRI) brain, followed by a computed tomography (CT) scan brain. The boy had various features of Goldenhar syndrome, e.g. cleft palate, absent right eye and ear, right mandibular hypoplasia, micrognathia, and preauricular tags. His developmental milestones were delayed. Airway evaluation showed Mallampati class II with limited movements of head and neck, which suggested possibility of difficult laryngoscopy and intubation. He had no vertebral anomalies or cardiac disease. A difficult airway continues to be a major cause of anaesthesia-related morbidity and mortality; and maintaining spontaneous breathing remains a vital technique in its management. Lack of anaesthesia-related complications with supraglottic devices encouraged us to present the advantage of utilising a laryngeal mask airway (LMA) under anaesthesia for successful management of predicted difficult airway.