The first and second branchial arch syndrome.
The first and second branchial arch syndrome.
复制标题
DOI：
10.1097/00006534-196511000-00001
复制
发表时间：
1965-11-01
影响因子：
3.6
通讯作者：
Grabb, W C
中科院分区：
文献类型：
--
作者：
Grabb, W C
第一和第二鳃弓综合征是由一系列先天畸形的面部结构组成的，这些面部结构起源于胚胎时期的第一和第二鳃弓，中间的第一咽袋和第一鳃裂，以及颞骨的原基（图1）。最充分表现为单侧或偶有双侧外耳、中耳、下颌、颧骨、上颌骨、颞骨、面部肌肉、咀嚼肌、腭肌、舌和腮腺发育不全，以及大口畸形和第一鳃裂窦（图2）。然而，通常情况下，完全综合征并不完全表达。
The first and second branchial arch syndrome is made up of a constellation of congenitally malformed facial structures which arise from the embryonic first and second branchial arches, the intervening first pharyngeal pouch and first branchial cleft, and the primordia of the temporal bone (fig. 1). In its fullest expression, a patient with this syndrome would exhibit unilateral or occasionally bilateral underdevelopment of the external ear, middle ear, man-dible, zygoma, maxilla, temporal bone, facial muscles, muscles of mastication, palatal muscles, tongue and parotid gland, as well as macrostomia and a first branchial cleft sinus (fig. 2). Frequently, however, the complete syndrome is not fully expressed.