Diagnosis and Management of Congenital Sensorineural Hearing Loss.
Diagnosis and Management of Congenital Sensorineural Hearing Loss.
复制标题
先天性感官听力损失的诊断和管理。
DOI：
10.1007/s40746-016-0056-6
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发表时间：
2016-09
影响因子：
--
通讯作者：
Oghalai JS
中科院分区：
文献类型：
--
作者：
Chen MM;Oghalai JS
Hearing loss is the most common sensory disorder in the USA. The diagnosis of congenital hearing loss starts with newborn hearing screening, which is best performed with auditory brainstem evoked responses in order to avoid the risk of missing auditory neuropathy spectrum disorder. A careful history and physical exam can occasionally help reveal the etiology for congenital hearing loss. Imaging studies, either CT temporal bones or MRI of the internal auditory canals without gadolinium, and genetic testing, in particular for connexin 26, connexin 30, and Pendred syndrome, are the most useful diagnostic tests. Management of congenital hearing loss involves early fitting of amplification. Early cochlear implantation, preferably before 2 years of age, should be strongly considered for children with bilateral severe hearing loss.
