Functional intestinal obstruction due to deficiency of argyrophil neurones in the myenteric plexus. Familial syndrome presenting with short small bowel, malrotation, and pyloric hypertrophy.
Functional intestinal obstruction due to deficiency of argyrophil neurones in the myenteric plexus. Familial syndrome presenting with short small bowel, malrotation, and pyloric hypertrophy.
复制标题
由于肌间神经丛中嗜银神经元缺乏而导致功能性肠梗阻。
DOI：
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复制
发表时间：
1976
影响因子：
5.2
通讯作者：
J. Lloyd
中科院分区：
文献类型：
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作者：
M. Tanner;B. Smith;J. Lloyd
在3例婴儿中，功能性肠梗阻与短小肠、旋转不良和幽门肥大相关，被证明是由于嗜银肌间神经丛发育失败所致，没有持续性肠梗阻。4例具有相似临床特征的婴儿，有证据表明该综合征为常染色体隐性遗传。
In 3 infants functional intestinal obstruction, associated with a short small intestine, malrotation, and pyloric hypertrophy, was shown to be due to failure of development of the argyrophil myenteric plexus, with the absence of ongoing peristalsis. 4 infants with similar clinical features have been described previously, and there is evidence for an autosomal recessive mode of inheritance of this syndrome.