DECLINING ELECTRICAL RESPONSE OF MUSCLE TO REPETITIVE NERVE-STIMULATION IN MYOTONIA
DECLINING ELECTRICAL RESPONSE OF MUSCLE TO REPETITIVE NERVE-STIMULATION IN MYOTONIA
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DOI：
10.1212/wnl.27.9.812
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发表时间：
1977-01-01
期刊：
影响因子：
9.9
通讯作者：
FADEN, AI
中科院分区：
文献类型：
--
作者：
AMINOFF, MJ;LAYZER, RB;FADEN, AI
研究了不同肌强直性疾病患者肌肉对重复神经刺激的电反应。递减反应是一种常见但并非恒定的发现，与严重程度或诊断无关。在整个刺激期间，这种递减要么持续，要么趋于平稳，有时随后是递增。如果它发生在低速率的刺激，更大的减量发生在较高的速率，通常在较短的潜伏期。它并不总是与存在的弱点，但在先天性肌强直患者更明显，并引起较低的刺激率时，短暂的弱点是一个功能的历史。
The electrical response of muscle to repetitive nerve stimulation was studied in patients with various myotonic disorders. A decrementing response was a common but not invariable finding, and was unrelated to the severity or diagnosis. The decrement either continued throughout the period of stimulation or leveled off, sometimes being followed by an increment. If it occurred at low rates of stimulation, a greater decrement occurred at higher rates, usually after a shorter latent period. It was not related consistently to the presence of weakness, but in patients with myotonia congenita it was more conspicuous and elicited by lower rates of stimulation when transient weakness was a feature of the history.