Angiosarcoma variant of Kasabach-Merritt syndrome
Angiosarcoma variant of Kasabach-Merritt syndrome
复制标题
DOI：
10.1097/00042737-200106000-00020
复制
发表时间：
2001-06-01
影响因子：
2.1
通讯作者：
Gontier, MF
中科院分区：
文献类型：
--
作者：
Alliot, C;Tribout, B;Gontier, MF
Kasabach-Merritt综合征的特点是发生弥散性血管内凝血（DIC），通常由良性血管瘤引起。在这里，我们报告的情况下，一个70岁的男子，其中DIC显示局部晚期肝肿瘤。虽然DIC与肝素，抗凝血酶III，新鲜冷冻血浆和皮质类固醇解决，病人死于腹腔积血跌倒后，3个月后，初步观察，尸检组织学检查允许诊断肝血管肉瘤。讨论了其病理生理机制和治疗方案。Eur J Gastroenterol Hepatol 13：731-734（C）2001 Lippincott威廉姆斯& Wilkins.
Kasabach-Merritt syndrome is characterized by the occurrence of disseminated intravascular coagulation (DIC) usually caused by benign angiomatous tumours, Here we report the case of a 70-year-old man in whom DIC revealed a locally advanced hepatic tumour. Although DIC resolved with heparin, antithrombin ill, fresh frozen plasma and corticosteroids, the patient died from haemoperitoneum following a fall, 3 months after the initial observation, Histopathological examination by autopsy allowed the diagnosis of hepatic angiosarcoma. The physiopathogenic mechanisms and treatment options are discussed. Eur J Gastroenterol Hepatol 13:731-734 (C) 2001 Lippincott Williams & Wilkins.