Upper airway and external genital involvement in epidermolysis bullosa dystrophica.
Upper airway and external genital involvement in epidermolysis bullosa dystrophica.
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营养不良性大疱性表皮松解症的上呼吸道和外生殖器受累。
DOI：
10.1148/radiology.143.2.7071344
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发表时间：
1982
期刊：
影响因子：
19.7
通讯作者：
McAlister,WH
中科院分区：
文献类型：
--
作者：
Shackelford,GD;Bauer,EA;Graviss,ER;McAlister,WH
影像学表现在两个病人的不常见表现的大疱性表皮营养不良的描述。一个女孩反复尿路感染有疤痕的外生殖器产生慢性阴道和子宫反流和尿潴留。第二个病人长期喘鸣被发现有声门下狭窄，由于局部声门下水肿与炎性膜。第二个病例说明了柱状上皮表面的偶尔参与，可以发生在营养不良性大疱性表皮和遗传性大疱性表皮。
Radiographic findings in two patients with uncommon manifestations of epidermolysis bullosa dystrophica are described. A girl with recurrent urinary tract infections had scarring of the external genitalia producing chronic vaginal and uterine reflux and retention of urine. A second patient with long-standing stridor was found to have subglottic narrowing due to localized subglottic edema associated with an inflammatory membrane. The second case illustrates the occasional involvement of columnar epithelial surfaces which can occur in both epidermolysis bullosa dystrophica and epidermolysis bullosa hereditaria letalis.