Partial blockage of sterol biosynthesis with a squalene synthase inhibltor in early postnatal Niemann-Pick type C npcnih null mice brains reduces neuronal cholesterol accumulation,abrogates astrogliosis,but may inhibit myelin maturation
Partial blockage of sterol biosynthesis with a squalene synthase inhibltor in early postnatal Niemann-Pick type C npcnih null mice brains reduces neuronal cholesterol accumulation,abrogates astrogliosis,but may inhibit myelin maturation
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用角鲨烯合酶抑制剂部分阻断出生后早期 Niemann-Pick C 型 npcnih 小鼠大脑中的甾醇生物合成,减少神经元胆固醇积累,消除星形胶质细胞增生,但可能抑制髓磷脂成熟
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发表时间:
2008
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et. al.
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作者:
Reid;P. C.;et. al.