PURE WORD DEAFNESS - ANALYSIS OF A CASE WITH BILATERAL LESIONS AND A DEFECT AT THE PRE-PHONEMIC LEVEL
PURE WORD DEAFNESS - ANALYSIS OF A CASE WITH BILATERAL LESIONS AND A DEFECT AT THE PRE-PHONEMIC LEVEL
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DOI：
10.1093/brain/105.2.271
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发表时间：
1982-01-01
期刊：
影响因子：
14.5
通讯作者：
ALBERT, ML
中科院分区：
文献类型：
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作者：
AUERBACH, SH;ALLARD, T;ALBERT, ML
纯词性耳聋是一种罕见的综合征，由 Kussmaul (1877) 首次描述，当时他使用术语“reinen WortaubheW”来描述无法理解口语单词的患者，但其言语产生和阅读能力却完好无损。临床上，纯词性耳聋患者应该不会出现任何失语症，尽管许多报告的病例都具有韦尼克失语症的特征（Brown，1974；Rubens，1979；Benson，1979）。该综合征与词性耳聋的症状不同，词性耳聋可能是韦尼克失语症的一个组成部分。一些作者更喜欢术语“语言听觉失认症”或“语言材料听觉失认症”（Ulrich，1978），但术语“纯词耳聋”保留了广泛的临床接受（Brown，1974；Hecaen和Albert，1978；Rubens，1979；Benson，1979）。目前还不确定纯言语性耳聋是否是一种明显的大脑功能障碍。 Wernicke 和 Freidlander (1893) 认为 Kussmaul 的案例代表了对其感觉性失语症的不完整描述。弗洛伊德（Freud，1891）怀疑周围性听力损失是孤立词性耳聋发生的必要条件。 Freund（1895）根据两个迷路功能障碍的病例得出结论，该综合征主要是由于听力损失造成的。 Marie（1906）也怀疑这种综合症的存在。然而，随后对几个有据可查的尸检病例的描述证实了该综合征是一个独特的实体（Goldstein，1974）。
PURE word deafness is a rare syndrome first described by Kussmaul (1877) when he used the term'reinen WortaubheW to describe a patient unable to comprehend spoken words with otherwise intact speech production and reading abilities. Clinically, the patient with pure word deafness is supposed to be free of any aphasic difficulties, although many of the reported cases are marked by elements of Wernicke's aphasia (Brown, 1974; Rubens, 1979; Benson, 1979). The syndrome is distinct from the symptom of word deafness which may appear as a component of Wernicke's aphasia. Some authors have preferred the term'verbal auditory agnosia'or'auditory agnosia for linguistic material'(Ulrich, 1978), but the term'pure word deafness' has retained wide clinical acceptance (Brown, 1974; Hecaen and Albert, 1978; Rubens, 1979; Benson, 1979). There was uncertainty that pure word deafness was a distinct disorder of cerebral function. Wernicke and Freidlander (1893) believed Kussmaul's case represented an incomplete description of his sensory aphasia. Freud (1891) suspected that a peripheral hearing loss was necessary for the development of an isolated word deafness. On the basis of two cases with labyrinthine dysfunction, Freund (1895) concluded that the syndrome was primarily due to hearing loss. Marie (1906) also doubted the existence of such a syndrome. However, the subsequent description of several well-documented cases which came to autopsy established the syndrome as a distinct entity (Goldstein, 1974).