A Case of Amyloidosis Presenting as Chronic Cholecystitis, Misdiagnosed as Polymyalgia Rheumatica.

A Case of Amyloidosis Presenting as Chronic Cholecystitis, Misdiagnosed as Polymyalgia Rheumatica.
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淀粉样变性表现为慢性胆囊炎误诊风湿性多肌痛一例。

DOI:
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发表时间:
2016
影响因子:
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通讯作者:
J. Kang
J. Kang
中科院分区:
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文献类型:
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作者:
Y. Um;Hyoun;Jin;Hundo Cho;J. Kang

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淀粉样变性是一种罕见的疾病,其特征是由错误折叠的蛋白质聚集而形成的无定形纤维状蛋白质在细胞外沉积。淀粉样变性局限于胆囊是不常见的,只有8例报告。我们描述了一个病例淀粉样变性诊断胆囊切除术,这可能也影响了肝脏和肾脏。患者被误诊为风湿性多肌痛,但在胆囊切除术治疗慢性胆囊炎后,我们最终诊断为淀粉样变性。我们回顾淀粉样变性病与胆囊受累的文献。
Amyloidosis is a rare disease defined by extracellular deposits of amorphous fibrillar proteins, derived from aggregations of misfolded proteins. Localization of amyloidosis in the gallbladder is uncommon; only eight cases have been reported. We describe a case of amyloidosis diagnosed by cholecystectomy, which possibly also affected the liver and kidney. The patient was misdiagnosed with polymyalgia rheumatica, but after a cholecystectomy to treat chronic cholecystitis, we ultimately diagnosed him with amyloidosis. We review amyloidosis with gallbladder involvement in the literature.