Japanese guidelines for diagnosis and treatment of junctional and dystrophic epidermolysis bullosa
Japanese guidelines for diagnosis and treatment of junctional and dystrophic epidermolysis bullosa
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DOI：
10.1007/s00403-002-0379-y
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发表时间：
2003-04-01
影响因子：
3
通讯作者：
Ogawa, H
中科院分区：
文献类型：
--
作者：
Tamai, K;Hashimoto, I;Ogawa, H
日本罕见难治性皮肤病研究小组致力于制定日本大疱性表皮病（EB）患者的诊断和治疗指南。这些指南特别针对EB的两种亚型，即连接型EB（JEB）和营养不良型EB（DEB），由于其严重性[1]，一直是政府努力促进该疾病基础和临床研究的重点。政府还将为特别是这两种EB亚型的患者提供财政援助。在这里，我们描述了JEB和DEB的建议指南，其中包括诊断标准，严重程度指数和治疗指南的现状。每个亚型的精确临床特征在本期其他地方描述。
The Japanese Study Group for Rare Intractable Skin Diseases has focused on establishing guidelines for the diagnosis and treatment of epidermolysis bullosa (EB) patients in Japan. These guidelines are designed particularly for two subtypes of EB, junctional EB (JEB) and dystrophic EB (DEB), that, due to their severity [1], have been the focus of the government’s efforts to promote basic and clinical research into this disease. The government is also forthcoming with financial aid for those afflicted with these two subtypes of EB in particular. Here, we describe the current status of the proposed guidelines for JEB and DEB which consist of a diagnostic standard, a severity index, and treatment guidelines. The precise clinical features of each subtype are described elsewhere in this issue.