Idiopathic pulmonary haemosiderosis: report of two cases and review of the literature.
Idiopathic pulmonary haemosiderosis: report of two cases and review of the literature.
复制标题
特发性肺含铁血黄素沉着症二例报告并文献复习。
DOI：
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发表时间：
1979
影响因子：
5.1
通讯作者：
Caixia Liu
中科院分区：
文献类型：
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作者：
Hongxia Ren;Liqiong Duan;Baohong Zhao;Xiao;Hongyi Zhang;Caixia Liu
特发性肺血色素沉着病（IPH）是一种罕见的疾病，主要影响儿童和青少年，通常是致命的。然而，越来越多的证据表明，这种情况的病因是免疫学的，免疫抑制剂可能延长缓解期。报告两例，其中一例具有吸收不良综合征的非典型特征。这在以前没有报道过。本文对文献进行了回顾，并对IPH的假设免疫学基础进行了讨论。
Idiopathic pulmonary haemosiderosis (IPH) is a rare disorder affecting mainly children and adolescents, and is usually fatal. However, there is increasing evidence that the aetiology of this condition is immunological, and that immunosuppressives may prolong remission. Two cases are reported, one of which has the atypical feature of a malabsorption syndrome. This has not been previously reported. The literature is reviewed and current ideas on the postulated immunological basis to IPH are discussed.