Surgical Correction of Crouzon Syndrome
Surgical Correction of Crouzon Syndrome
复制标题
克鲁宗综合征的手术矫正
DOI：
10.1097/00006534-199003000-00002
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发表时间：
1990
影响因子：
3.6
通讯作者：
R. Sheen
中科院分区：
文献类型：
--
作者：
D. David;R. Sheen
本文分析了39例Crouzon综合征的外科治疗结果。早期的额眶前移和颅骨切除术在缓解颅内压升高和减少眼球突出方面普遍成功。然而，最终的美容矫正没有实现，早期的颅骨手术不能防止面中部发育不全的发展。在30名患者中进行了32次面中部推进。16例患者术后随访时间超过2年。所有患者均获得了满意的术后早期结果。在长期随访组中，11例患者保持了满意的外观，而5例出现复发畸形。分析表明，这与手术时年龄较小和下颌骨持续生长有关。成人额面前移术可获得良好的长期效果，但并发症发生率较高。
This study analyzes the results of surgical treatment in 39 patients with the Crouzon syndrome. Early frontoorbital advancement and craniectomy were universally successful in relieving raised intracranial pressure and in reducing ocular proptosis. However, definitive cosmetic correction was not achieved, and early cranial surgery was not able to prevent the development of midface hypoplasia. Thirty-two midfacial advancements have been performed in 30 patients. Sixteen patients had sufficient follow-up data for more than 2 years postoperatively. In all patients, a satisfactory early postoperative result was achieved. In the long-term follow-up group, 11 patients have maintained a satisfactory appearance, while 5 have developed recurrent deformity. Analysis shows this to be associated with a younger age at operation and continued mandibular growth. Frontofacial advancement in adults achieves good long-term results but is associated with a higher incidence of complications.