Late presentation, MR imaging features an surgical treatment of Herlyn-Werner- Wunderlich syndrome (classification 2.2); a case report
Late presentation, MR imaging features an surgical treatment of Herlyn-Werner- Wunderlich syndrome (classification 2.2); a case report
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DOI：
10.1186/s12905-018-0655-4
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发表时间：
2018-10-03
影响因子：
2.5
通讯作者：
Haidary, Nilab
中科院分区：
文献类型：
--
作者：
Hamidi, Hidayatullah;Haidary, Nilab
背景：Herlyn-Werner-Wunderlich综合征是一种非常罕见的先天性泌尿生殖系统畸形，以子宫发育迟缓、半阴道失明和同侧肾发育不全为特征。病例介绍：作者报告一例19岁未婚妇女的Herlyn-Werner-Wunderlich综合征，表现为盆腔疼痛和盆腔肿块。MRI显示双侧子宫、右半阴道阻塞和同侧肾发育不全的典型特征。患者随后接受了手术。结论：单侧无肾和盆腔肿块的患者可怀疑为Herlyn-Werner-Wunderlich综合征。超声和磁共振成像可以很好地显示疾病的实质，手术是治疗半阴道阻塞的首选方法。
Background: Herlyn-Werner-Wunderlich syndrome is a very rare congenital genitourinary anomaly characterized by uterus didelphys, blind hemivagina and ipsilateral renal agenesis.Case presentation: Authors present a case of Herlyn-Werner-Wunderlich syndrome in a 19-year-old unmarried woman who presented with pelvic pain and pelvic mass. MR imaging revealed the typical features of didelphys uterus, obstructed right hemivagina and ipsilateral renal agenesis. The patient subsequently underwent surgery.Conclusions: Herlyn-Werner-Wunderlich syndrome would be suspected in patients with unilateral absent kidney and pelvic mass. Ultrasonography and MR imaging can well depict the disease entity and surgery is the treatment of choice for obstructed hemivagina.