Epignathus with fetiform features.
Epignathus with fetiform features.
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DOI：
10.4103/0974-2727.78571
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发表时间：
2011-01
影响因子：
1.1
通讯作者：
Sitaram A
中科院分区：
文献类型：
--
作者：
Kumar SY;Shrikrishna U;Shetty J;Sitaram A
上颌骨畸胎瘤是一种非常罕见的口咽畸胎瘤，通常发生在上颚，由于新生儿时期的气道阻塞，导致高死亡率（80-100%）。我们报告一位28周的早产男婴，发生于上颌骨的胎儿状未成熟畸胎瘤，出生后立即死亡。由于上颌骨在分娩时是一种危及生命的疾病，因此产前诊断对于协调治疗和适当的管理至关重要，通过气管插管或气管切开术保护气道，然后完全切除肿瘤。
Epignathus is an extremely rare oropharyngeal teratoma that commonly arises from the palate, leading to a high mortality (80–100%) due to airway obstruction in the neonatal period. We present a case of epignathus immature teratoma with fetiform features, originating from basisphenoid in a 28-week preterm male baby, who succumbed to death immediately after birth. Since epignathus is a life-threatening condition at the time of delivery, a prenatal diagnosis is essential to coordinate the treatment and appropriate management by securing the airway, either by endotracheal intubation or tracheostomy followed by complete resection of the tumor.