Congenital Budd-Chiari syndrome.
Congenital Budd-Chiari syndrome.
复制标题
先天性布加综合征。
DOI：
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发表时间：
1983
期刊：
影响因子：
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通讯作者：
E. Yunis
中科院分区：
文献类型：
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作者：
R. Jaffe;E. Yunis
Budd-Chiari综合征是由于肝静脉或肝口血栓性闭塞引起的，在婴儿中并不常见。文献回顾显示，没有记录的病例在出生时有症状。我们描述了一个男婴腹水目前在出生时。7周龄时肝活检显示肝窦扩张，但仅在4个月后尸检时诊断为布-加综合征。虽然怀疑母亲滥用药物，但原因尚未确定。
Budd-Chiari syndrome, due to thrombotic occlusion of hepatic veins or ostia, is unusual in infants. Review of the literature reveals no documented case symptomatic at birth. We describe a male infant with ascites present at birth. A liver biopsy at 7 weeks of age showed sinusoidal dilatation, but the diagnosis of Budd-Chiari syndrome was made only at autopsy, 4 months later. The cause was not determined although maternal drug abuse was suspected.