WORD DEAFNESS - 100 YEARS LATER
WORD DEAFNESS - 100 YEARS LATER
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DOI：
10.1136/jnnp.49.5.489
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发表时间：
1986-05-01
影响因子：
11
通讯作者：
SCHWARTZ, M
中科院分区：
文献类型：
--
作者：
BUCHMAN, AS;GARRON, DC;SCHWARTZ, M
自最初描述以来，单词聋的诊断已大大扩展。关于纯词聋、听觉失认症和皮质性聋等相关术语的使用出现了混淆。本文报告三例新的字聋病例，其中一例有CT和尸检对照。这些情况下，与34例以前报道的各种皮质听觉障碍。我们的回顾表明，对语言和非语言声音理解和音乐能力进行正式测试的单词性耳聋患者总是表现出更普遍的听觉失认症。尽管有听觉缺陷和相关的语言异常的频谱，文字聋患者有共同的特点，包括病因，病理，临床表现和过程。这些共同的特征证明了将异质性皮质听觉障碍包括在词聋的范畴内是合理的。尽管有一些局限性，术语“词聋”应保留这种综合征，因为无法理解口语是最明显的临床缺陷。言语性耳聋最常由心源性栓塞引起的脑血管意外引起，伴有双颞叶皮质下损害。脑损伤的顺序并不能预测由此产生的听觉缺陷。音乐能力的损害与听觉障碍的严重程度相当。
Since its original description the diagnosis of word deafness has been greatly expanded. Confusion has arisen with regard to the usage of the related terms pure word deafness, auditory agnosia, and cortical deafness. Three new cases of word deafness are presented including one case with CT and necropsy correlation. These cases are compared with 34 previously reported cases of various cortical auditory disorders. Our review establishes that patients with word deafness who have had formal testing of linguistic and non-linguistic sound comprehension and musical abilities always demonstrated a more pervasive auditory agnosia. Despite the spectrum of auditory deficits and associated language abnormalities, patients with word deafness share common features including aetiology, pathology, clinical presentation and course. These common features justify inclusion of heterogeneous cortical auditory disorders under the rubic of word deafness. Despite some limitations the term "word deafness" should be retained for this syndrome, since inability to comprehend spoken words is the most distinctive clinical deficit. Word deafness is most frequently caused by cerebrovascular accidents of presumed cardiac embolisation, with bitemporal corticosubcortical lesions. The sequence of cerebral injury is not predictive of resulting auditory deficits. Impairment of musical abilities parallels the severity of the auditory disorder.