Recurrent unexplained lipothymia: do not forget the capillary leak syndrome
Recurrent unexplained lipothymia: do not forget the capillary leak syndrome
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DOI：
10.1016/j.revmed.2007.01.020
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发表时间：
2007-10-01
影响因子：
0.9
通讯作者：
Colle, B.
中科院分区：
文献类型：
--
作者：
Debourdeau, P.;Bory, P.;Colle, B.
导论. - 全身性毛细血管渗漏综合征（SCLS）是一种罕见的疾病，其特征是由于血浆从血管内明显转移到血管外空间而反复自发发作的低血容量休克。它表现为低血压、血液浓缩和低白蛋白血症的特征性三联征。病例报告。- 我们描述了一个SCLS患者复发性脂血症谁提出了第一次迟发性水肿，被认为是由于奥利司他治疗。在第二次发作时，当血浆返回血管时，患者出现肺动脉高压。第三次特征三联征导致了SCL的诊断。讨论。- 对于原因不明的复发性低血容量性休克，应考虑SCLS的鉴别诊断。然而，症状可能仅限于单纯性脂血症或一过性水肿或迟发性低Alburninemia，使诊断困难。(C)2007年，Elsevier Masson SAS。图斯所有权保留。
Introduction. - Systemic capillary leak syndrome (SCLS) is a rare disorder characterized by recurrent spontaneous episodes of hypovolaernic shock due to marked plasma shifts from the intravascular to the extravascular space. It presents as the characteristic triad of hypotension, haemoconcentration and hypoalbuminemia.Case report. - We describe a patient with SCLS with recurrent lipothymia who presented first with delayed oedema that was thought to be due to orlistat treatment. On the second episode the patient was seen with a pulmonary hypertension when plasma came back into vessels. On the third time the characteristic triad led to the diagnosis of SCLS.Discussion. - SCLS should be considered in the differential diagnosis of recurrent hypovolemic shock without identifiable cause. Nevertheless, symptoms may be restricted to sole lipothymia or transient oedema or delayed hypoalburninemia rendering the diagnosis difficult. (C) 2007 Elsevier Masson SAS. Tous droits reserves.