Hepatic angiomyolipoma with early drainage veins into the hepatic and portal vein
Hepatic angiomyolipoma with early drainage veins into the hepatic and portal vein
复制标题
早期引流静脉进入肝和门静脉的肝血管平滑肌脂肪瘤
DOI：
10.1007/s12328-019-00946-2
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发表时间：
2019
影响因子：
1
通讯作者：
Takeuchi Hiroya
中科院分区：
文献类型：
--
作者：
Kiuchi Ryota;Sakaguchi Takanori;Kitajima Ryo;Furuhashi Satoru;Takeda Makoto;Hiraide Takanori;Morita Yoshifumi;Ushio Takasuke;Ishikawa Rei;Baba Satoshi;Takeuchi Hiroya
肝血管平滑肌脂肪瘤(AML)是一种罕见的间质肿瘤，由厚壁血管、平滑肌肉和脂肪组织组成。肝脏AML的一种特殊的放射学表现是通过增强计算机断层扫描(CT)发现的早期引流静脉。我们报告一例肝脏急性髓细胞白血病，显示早期引流静脉同时进入肝静脉和门静脉。该病例涉及一名46岁的女性，她因巨大的肝脏肿瘤而转诊至本院。CT显示左叶和右叶分别有14厘米和1厘米的强化肿瘤。磁共振成像显示较大的肿瘤中存在脂肪组织。肝动脉造影显示早期引流静脉同时流入肝静脉和门静脉。根据肝脏AML的诊断，行左肝切除和部分肝切除。病理显示这两种肿瘤都是基于人类黑色素瘤BLACK-45免疫阳性的肝脏AML。肝性AML早期引流静脉同时进入肝静脉和门静脉的情况很少见。扩张和逆行的静脉引流了肿瘤丰富的动脉血流。早期发现肝静脉和门静脉引流静脉有助于肝AMLS的诊断。
Hepatic angiomyolipoma (AML) is a rare stromal tumor composed of variable admixtures of thick-walled vessels, smooth muscles and adipose tissue. One of the specific radiological findings of hepatic AML is an early drainage vein noted via enhanced computed tomography (CT). We report a case of hepatic AML showing early drainage veins into both the hepatic and portal vein. The case involved a 46-year-old woman who was referred to our hospital because of a giant hepatic tumor. CT revealed well-enhanced 14 cm and 1 cm tumors in the left and right lobes, respectively. Magnetic resonance imaging demonstrated the existence of adipose tissues in the larger tumor. Hepatic arteriography revealed early drainage veins draining into both the hepatic and portal vein. Based on a diagnosis of hepatic AML, left hepatectomy and partial hepatectomy were performed. Pathology revealed both tumors as hepatic AML based on human melanoma black-45 immuno-positivity. Hepatic AML with early drainage veins into both the hepatic and portal vein is rare. The dilated and retrogressive vein drains the abundant arterial blood flow of the tumor. The finding of early drainage veins into not only the hepatic vein but also the portal vein should be helpful for diagnosing hepatic AMLs.