Congenital Langerhans cell histiocytosis: the self-healing variety.
Congenital Langerhans cell histiocytosis: the self-healing variety.
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先天性朗格汉斯细胞组织细胞增多症：自愈型。
DOI：
10.1097/00043426-200406000-00014
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发表时间：
2004
期刊：
影响因子：
--
通讯作者：
R. Mehta
中科院分区：
文献类型：
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作者：
Mandeep Walia;P. Paul;S. Mishra;R. Mehta
先天性自愈性朗格汉斯细胞组织细胞增多症（CSHLCH）是朗格汉斯细胞组织细胞增多症的一种罕见的变体，在出生或新生儿时期表现为自发的皮肤病变。受影响的婴儿在其他方面都很好，没有全身性疾病。本文描述了一例CSHLCH，可能是印度的第一例病例报告。患者在出生第三天出现全身多发丘疹样病变，无全身受累。病变在6个月大时自发消退，1岁时无复发迹象。虽然CSHLCH是一种良性和自限性疾病，但强调长期随访以寻找复发证据。
Congenital self-healing Langerhans cell histiocytosis (CSHLCH) is a rare variant of Langerhans cell histiocytosis, presenting at birth or in the neonatal period with cutaneous lesions that involute spontaneously. Affected infants are otherwise well with no systemic illness. A case of CSHLCH, probably the first case report from India, is described. The patient presented on the third day of life with multiple papulonodular lesions over the body, with no systemic involvement. The lesions spontaneously regressed by 6 months of age, with no evidence of relapse at 1 year of age. Although CSHLCH is a benign and self-limited condition, long-term follow-up for evidence of relapse is emphasized.