Primary Cardiac Angiosarcoma in a Young Woman
Primary Cardiac Angiosarcoma in a Young Woman
复制标题
DOI：
10.1159/000273112
复制
发表时间：
2010-01-01
影响因子：
0.8
通讯作者：
Mariotta, Salvatore
中科院分区：
文献类型：
--
作者：
Pezzuto, Aldo;Gencarelli, Giorgia;Mariotta, Salvatore
一位30岁的女性因严重呼吸急促而入院。经胸超声心动图显示中度心包积液伴右心房病变，经胸部CT扫描和心脏RMN证实。胸膜和中叶受累发生在一个月内。病理检查证实为转移性血管肉瘤。两个月后，由于复发性胸腔积液，进行了化学胸膜固定术。开始化疗，但患者在诊断后四个月死亡。本病例强调了心脏血管肉瘤在最初临床表现、可用诊断方法和治疗选择方面的误诊。
A 30-year-old woman was admitted to our hospital with severe shortness of breath. A transthoracic echocardiogram showed moderate pericardial effusion with a lesion in the right atrium, confirmed by chest CT scan and cardiac RMN. Pleural and middle lobe involvement occurred within one month. Middle lobe biopsy was performed and pathological examination confirmed the diagnosis of metastatic angiosarcoma. After two months, because of recurrent pleural effusions, chemical pleurodesis was performed. Chemotherapy was started but the patient died four months after the diagnosis. This case highlights the misdiagnosis at initial clinical presentation, available diagnostic approaches and therapeutic options for cardiac angiosarcoma.