Bisoprolol treatment for cyanotic spells--a 69-year-old female with uncorrected pentalogy of Fallot.
Bisoprolol treatment for cyanotic spells--a 69-year-old female with uncorrected pentalogy of Fallot.
复制标题
比索洛尔治疗紫绀型发作——一名 69 岁女性，患有未矫正的法洛五联症。
DOI：
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复制
发表时间：
2001
影响因子：
4.2
通讯作者：
S. Fuchshuber
中科院分区：
文献类型：
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作者：
H. Anders;S. Fuchshuber
法洛四联症是一种罕见的紫绀型先天性心脏病，其特征是主动脉双心室起源于巨大的室间隔缺损上方，肺动脉流出道阻塞，右心室肥大（法洛四联症）和房间隔缺损。由于晕厥、心律失常或充血性心力衰竭导致的死亡率在10岁时约为75%，在40岁时约为97%。我们报告一位69岁的女性，患有未矫正的法洛五联症，在典型的紫绀发作期间反复发作晕厥。比索洛尔治疗被推荐用于有症状的儿童，也改善了我们患者的症状。我们的结论是，法洛五联症的单一患者达到第七个十年，紫绀型先天性心脏病是一种罕见的原因晕厥的老年人。
Pentalogy of Fallot is a rare cyanotic congenital heart disease characterized by biventricular origin of the aorta above a large ventricular septal defect, obstruction of the pulmonary outflow, right ventricular hypertrophy (tetralogy of Fallot), and an atrial septal defect. Mortality due to syncope, arrhythmia or congestive heart failure is about 75% by the age of 10 years and 97% by the age of 40. We report a 69-year old female with uncorrected pentalogy of Fallot who suffered from recurrent syncope during classic cyanotic spells. Treatment with bisoprolol is recommended in symptomatic children and also improved symptoms in our patient. We conclude that single patients with pentalogy of Fallot reach the seventh decade and that cyanotic congenital heart disease is a rare cause of syncope in the elderly.