[A case of pulmonary alveolar proteinosis presenting with peripheral infiltrates].
[A case of pulmonary alveolar proteinosis presenting with peripheral infiltrates].
复制标题
伴有周围浸润的肺泡蛋白沉积症一例[J].
DOI：
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发表时间：
1999
期刊：
影响因子：
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通讯作者：
H. Nakamura
中科院分区：
文献类型：
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作者：
N. Inui;K. Chida;T. Suda;M. Toyoshima;A. Todate;K. Ide;K. Tsukamoto;J. Sato;T. Tsuchiya;H. Nakamura
我们报告一例肺泡蛋白沉积症（PAP）。一名39岁无症状女性因胸部X线片出现异常阴影入院。胸部 X 光片显示双肺周围有浸润。计算机断层扫描显示斑片状周边毛玻璃衰减，集中于胸膜下。支气管肺泡灌洗液清澈。由于经支气管肺活检结果尚无定论，因此进行了 VATS 活检。样本显示蛋白质物质在肺泡腔内积累。该患者被诊断为 PAP。尽管 PAP 患者的放射学阴影分布各不相同，但肺门周围或集中阴影通常占主导地位。在我们的患者中，肺部的胸膜下区域几乎全部受到影响。
We report a case of pulmonary alveolar proteinosis (PAP). A 39-year-old asymptomatic woman was admitted to our hospital because of abnormal shadows on chest X-ray films. Chest X-ray films revealed peripheral infiltrates in both lungs. Computed tomographic examination showed patchy peripheral ground-glass attenuation, concentrated subpleurally. Bronchoalveolar lavage fluid was clear. Because transbronchial lung biopsy findings were inconclusive, a VATS-biopsy was performed. The specimens demonstrated accumulation of proteinaceous materials within alveolar spaces. The patient was given a diagnosis of PAP. Although the distribution of radiographic shadows varies in patients with PAP, perihilar or centralized shadows usually predominate. In our patient, subpleural areas of the lung were affected almost exclusively.