Dentomaxillofacial characteristics of ectodermal dysplasia.
Dentomaxillofacial characteristics of ectodermal dysplasia.
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外胚层发育不良的牙颌面特征。
DOI：
10.1111/cga.12073
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发表时间：
2015
期刊：
影响因子：
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通讯作者：
Moriyama K
中科院分区：
文献类型：
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作者：
Nakayama Y;Baba Y;Tsuji M;Fukuoka H;Ogawa T;Ohkuma M;Moriyama K
这项回顾性医院研究的目的是阐明外胚层发育不良的牙颌面特征。6名日本人（1名男性和5名女性;年龄范围，12.7-27.2岁）接受了全面检查，包括病史记录、头影测量分析、全景X线摄影和牙模型分析。所有受试者均具有两种或两种以上临床诊断外胚层发育不良的主要表现（例如，毛发、牙齿、指甲和汗腺缺陷）。他们表现为缺牙（平均缺牙数，9.5;范围，5-14），特别是在前磨牙区域，和釉质发育不良。5例受试者双侧磨牙咬合，1例受试者单侧磨牙咬合。常见的骨骼特征是面高小、上颌骨发育不全、下颌骨逆时针旋转和下颌前突。有趣的是，上颌第一磨牙位于较高的位置和上前面部高度小于日本正常。结果表明，垂直和前后上颌生长迟缓，而不是缺乏咬合支持，由于缺牙，导致减少前面部高度的个人与外胚层发育不良。
The aim of this retrospective hospital‐based study was to elucidate the dentomaxillofacial characteristics of ectodermal dysplasia. Six Japanese individuals (one male and five female; age range, 12.7–27.2 years) underwent comprehensive examinations, including history recording, cephalometric analysis, panoramic radiography, and analysis of dental models. All the subjects had two or more major manifestations for clinical diagnosis of ectodermal dysplasia (e.g., defects of hair, teeth, nails, and sweat glands). They presented hypodontia (mean number of missing teeth, 9.5; range, 5–14), especially in the premolar region, and enamel dysplasia. Five subjects had bilateral molar occlusion, whereas one subject had unilateral molar occlusion. The common skeletal features were small facial height, maxillary hypoplasia, counterclockwise rotation of the mandible, and mandibular protrusion. Interestingly, the maxillary first molars were located in higher positions and the upper anterior facial height was smaller than the Japanese norm. The results suggest that vertical and anteroposterior maxillary growth retardation, rather than lack of occlusal support due to hypodontia, leads to reduced anterior facial height in individuals with ectodermal dysplasia.