Congenital aganglionosis of the entire colon in neonates.
Congenital aganglionosis of the entire colon in neonates.
复制标题
新生儿先天性全结肠无神经节病。
DOI：
10.1259/0007-1285-49-577-27
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发表时间：
1976
期刊：
影响因子：
--
通讯作者：
R. Golding
中科院分区：
文献类型：
--
作者：
B. Cremin;R. Golding
新生儿X线诊断及六例报告。全结肠无神经节细胞症（TCA）是一种通常称为长段先天性巨结肠的疾病。这不是一种罕见的情况，但往往是不被承认的。它有很高的死亡率，经常并发小肠结肠炎。所有表现为梗阻性结肠病变的婴儿，应怀疑结肠部分无神经节细胞症。在TCA中，钡灌肠的改变很容易被认为是不显著的。然而，检查期间的游离回肠反流，在回肠中有一个过渡点，以及检查后整个结肠中的钡剂滞留，都是诊断性的。
A report of six cases and their radiological diagnosis in neonates. Total colonic aganglionosis (TCA) is a variety of what is commonly known as long segment Hirschsprung's disease. This is not a rare condition, but is often unrecognized. It has a high mortality, frequently with a complicating enterocolitis. Aganglionosis of some part of the colon should be suspected in all babies who show obstructive plain film changes. In TCA the barium enema changes may easily be passed as unremarkable. However, free ileal reflux during the examination, with a transition point in the ileum, and retention of barium in the entire colon after the examination, are diagnostic.