Primitive Myxoid Mesenchymal Tumor of Infancy Involving Chest Wall in an Infant: A Case Report and Clinicopathologic Correlation
Primitive Myxoid Mesenchymal Tumor of Infancy Involving Chest Wall in an Infant: A Case Report and Clinicopathologic Correlation
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DOI：
10.2350/15-05-1644-cr.1
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发表时间：
2016-05-01
影响因子：
1.9
通讯作者：
Chintagumpala, Murali
中科院分区：
文献类型：
--
作者：
Foster, Jennifer H.;Vasudevan, Sanjeev A.;Chintagumpala, Murali
婴儿原始粘液样间叶肿瘤（PMMTI）是一种罕见的儿童早期间叶肿瘤，其特征是周围结构的侵袭性局部浸润，罕见的转移，以及对化疗的反应差。由于缺乏转移的偏好和对传统化疗的不良反应，单独手术似乎是最有效的治疗方法。下面，我们报告了一名PMMT 1患者，通过手术和观察成功治疗，并总结了现有文献中关于该病变的组织病理学特征和治疗。
Primitive myxoid mesenchymal tumor of infancy (PMMTI) is a rare mesenchymal tumor of early childhood characterized by aggressive local infiltration of surrounding structures, rare metastases, and poor response to chemotherapy. Surgery alone appears to be the most effective treatment given the lack of predilection for metastasis and poor response to traditional chemotherapy. Below we report a patient with PMMT1 successfully managed with surgery and observation and summarize the existing literature on histopathologic features and treatment of this lesion.