DIFFUSE INTERSTITIAL LUNG-DISEASE IN NEUROFIBROMATOSIS
DIFFUSE INTERSTITIAL LUNG-DISEASE IN NEUROFIBROMATOSIS
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DOI：
10.1097/00007611-198608000-00007
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发表时间：
1986-08-01
影响因子：
1.1
通讯作者：
MCCAY, MB
中科院分区：
文献类型：
--
作者：
BURKHALTER, JL;MORANO, JU;MCCAY, MB
神经纤维瘤病与弥漫性间质性肺病的关系被认为是存在的，尽管对它的大规模研究相对较少。肺部表现包括弥漫性间质纤维化或大疱形成，或两者兼而有之。我们对这一疾病过程的10年经验表明，在我们的神经纤维瘤病患者中，弥漫性间质性肺病的发病率略低于7%。我们包括一个神经纤维瘤病和弥漫性肺疾病的病例，在下叶大疱的形成有点不寻常，与其明显的上叶优势形成对比。
An association of neurofibromatosis with diffuse interstitial lung disease is thought to exist, though there have been relatively few large studies of it. The pulmonary manifestations consist of diffuse interstitial fibrosis or formation of bullae, or a combination of both. Our experience with this disease process during a ten-year period shows slightly less than a 7% incidence of diffuse interstitial lung disease in our patients with neurofibromatosis. We include a case of neurofibromatosis and diffuse lung disease that is somewhat unusual in the formation of bullae in the lower lobe, in contradistinction to its marked upper lobe predominance.