Fetal Epignathus: The Case of an Early EXIT (Ex Utero Intrapartum Treatment)
Fetal Epignathus: The Case of an Early EXIT (Ex Utero Intrapartum Treatment)
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胎儿内颌畸形：早期退出（宫外产时治疗）的案例
DOI：
10.1097/aog.0b013e318242b3f1
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发表时间：
2012
影响因子：
7.2
通讯作者：
C. Major
中科院分区：
文献类型：
--
作者：
J. Chung;Christine K. Farinelli;M. Porto;C. Major
背景：胎儿上颌畸形是一种源自口咽部的畸胎瘤，可能致命，可以在产前诊断出来。病例：一名 29 岁女性，1 号孕妇，经评估甲胎蛋白水平升高。影像学评估显示胎儿上颌骨无颅内延伸。早产需要在妊娠 27 5/7 周时使用经典切口进行宫外产时治疗 (EXIT) 程序进行分娩。新生儿体型较小，脐带较短，需要完全外露以确保呼吸道通畅。病理学检查发现未成熟畸胎瘤。结论：胎儿上颌骨的产前诊断是必要的，以便可以讨论所有的选择。出生时气道管理可能需要执行 EXIT 程序。如果需要早产，子宫切口的选择和胎儿大小是成功结果需要考虑的重要因素。
BACKGROUND: Fetal epignathus, a teratoma arising from the oropharynx that may be lethal, can be diagnosed prenatally. CASE: A 29-year-old woman, gravida 1, was evaluated for an elevated alpha-fetoprotein level. Imaging evaluation revealed a fetal epignathus without intracranial extension. Preterm labor necessitated delivery at 27 5/7 weeks of gestation with ex utero intrapartum treatment (EXIT) procedure using a classical incision. The neonate's small size and short umbilical cord required complete exteriorization to secure the airway. Pathology revealed an immature teratoma. CONCLUSION: Prenatal diagnosis of fetal epignathus is imperative so that all options can be discussed. An EXIT procedure may be necessary for airway management at birth. If preterm delivery is necessary, choice of uterine incision and fetal size are important factors to consider for a successful outcome.