Urticaria as a presenting manifestation of adult-onset Still's disease
Urticaria as a presenting manifestation of adult-onset Still's disease
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DOI：
10.1007/s100670070034
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发表时间：
2000-01-01
影响因子：
3.4
通讯作者：
Maestrini, MD
中科院分区：
文献类型：
--
作者：
Salaffi, F;Filosa, G;Maestrini, MD
成人斯蒂尔病是一种病因不明的罕见疾病，其特征是高热、一过性皮疹、斑丘疹、关节痛或关节炎、淋巴结病、肝脾肿大、咽喉痛和浆膜炎。它与明显的白细胞增多、红细胞沉降率高、血清铁蛋白水平升高以及类风湿因子和抗核抗体试验阴性有关。在这里，我们报告一个病人，其中荨麻疹样皮疹是一种罕见的AOSD的临床表现。据我们所知，这种关联以前只报道过一次。
Adult-onset Still's disease (AOSD) is a rare disorder of unknown aetiology, characterised by high spiking fever, an evanescent, erythematous, maculopapular rash, arthralgia or arthritis, lymphadenopathy, hepatosplenomegaly, sore throat and serositis. It is associated with marked leukocytosis, high erythrocyte sedimentation rate, increased level of serum ferritin and negative rheumatoid factor and antinuclear antibody tests. Here we report a patient in whom an urticaria-like rash was an uncommon presenting clinical feature of AOSD. To our knowledge, this association has only been reported once before.