Thoracic lymphangiomatosis in a child
Thoracic lymphangiomatosis in a child
复制标题
DOI：
10.1097/00043426-200402000-00018
复制
发表时间：
2004-02-01
影响因子：
1.2
通讯作者：
Zuppan, CW
中科院分区：
文献类型：
--
作者：
Alvarez, OA;Kjellin, I;Zuppan, CW
一个8岁的男孩表现为纵隔肿块，肺浸润，弥散性血管内凝血被诊断为淋巴管瘤病。尽管进行了医疗管理，他还是出现了多器官衰竭，最终死亡。作者讨论了诊断结果、医疗管理和病理，并回顾了文献中另外52例胸部淋巴管瘤病。患者表现为乳糜胸（49%）、肿块（47%）、肺浸润（45%）、骨病变（39%）、脾病变（19%）、颈椎受损伤（15%）、弥散性血管内凝血（9%）和皮肤受损伤（7%）。儿童(
An 8-year-old boy who presented with a mediastinal mass, pulmonary infiltrates, and disseminated intravascular coagulation was diagnosed with lymphangiomatosis. Despite medical management, he developed multiple organ failure and died. The authors discuss the diagnostic findings, medical management, and pathology and review 52 additional cases of thoracic lymphangiomatosis from the literature. Patients presented with chylothorax (49%), a mass (47%), pulmonary infiltrates (45%), bone lesions (39%), splenic lesions (19%), cervical involvement (15%), disseminated intravascular coagulation (9%), and skin involvement (7%). Children (