ATYPICAL BENIGN PARTIAL EPILEPSY OF CHILDHOOD
ATYPICAL BENIGN PARTIAL EPILEPSY OF CHILDHOOD
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DOI：
10.1111/j.1469-8749.1982.tb13620.x
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发表时间：
1982-01-01
影响因子：
3.8
通讯作者：
CHEVRIE, JJ
中科院分区：
文献类型：
--
作者：
AICARDI, J;CHEVRIE, JJ
本文报告7例少见癫痫综合征患儿。每个患者的主要临床特征包括在2.5-6岁之间起病，出现几种类型的癫痫(特别是部分运动发作、不典型的缺席和肌肉紧张性癫痫)，并在整个过程中保持正常的神经和精神功能。脑电图像的特征是清醒记录和睡眠痕迹之间的鲜明对比，清醒记录通常显示局灶性发作，睡眠痕迹显示几乎连续的、弥漫的、缓慢的棘波活动。虽然电临床特征提示为Lennox-Gastaut综合征或肌阵挛癫痫，但年龄最大的5例患者癫痫发作自发缓解，最年轻的2例患者癫痫发作完全缓解。讨论了这些非典型良性部分性癫痫的临床和脑电特征，以区别于更严重的儿童期肌紧张性癫痫综合征。
Seven children with an unusual epileptic syndrome are reported. The main clinical features in each patient included onset between 2.5-6 yr of age, the occurrence of several types of seizure (especially partial motor fits, atypical absences and myo-atonic seizures), and the persistance of normal neurological and mental function throughout the course. The EEG picture was characterized by a striking contrast between waking records, which usually displayed focal paroxysms, and sleep tracings which showed an almost continuous, diffuse, slow spike-wave activity. Although the electroclinical features suggested the diagnosis of Lennox-Gastaut syndrome or myoclonic epilepsy, the seizures remitted spontaneously in the 5 oldest patients and could well do so in the 2 youngest ones. The clinical and electroencephalographic features that permit these cases of atypical benign partial epilepsy to be distinguished from the more severe myoatonic epileptic syndromes of childhood are discussed.