Dental root abnormalities in four children with PHACE syndrome.
Dental root abnormalities in four children with PHACE syndrome.
复制标题
四名 PHACE 综合征儿童的牙根异常。
DOI：
10.1111/pde.13818
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发表时间：
2019
影响因子：
1.5
通讯作者：
Hodgson,BrianD
中科院分区：
文献类型：
--
作者：
Youssef,MollyJ;Siegel,DawnH;Chiu,YvonneE;Drolet,BethA;Hodgson,BrianD
PHACE（S）综合征是一种以后颅窝畸形、血管瘤、动脉异常、心脏缺陷、眼睛异常、胸骨裂和脐上缝为特征的疾病。我们报告四位患有PHACE（S）症候群的儿童，他们的第一恒磨牙牙根缺失或严重畸形。儿童磨牙的牙根异常是双侧的，并不局限于皮肤血管瘤影响的部分。牙根异常的原因尚不清楚，但考虑到这些发现在健康儿童中的罕见性，这可能是PHACE综合征的额外牙科表现。功能性根在PFMs中的缺乏可能导致显著的后果。因此，我们建议PHACE综合征儿童在过渡牙列期进行全景牙科X线片检查，以筛查牙根异常。
PHACE(S) syndrome is a condition characterized by posterior fossa malformations, hemangiomas, arterial anomalies, cardiac defects, eye abnormalities, sternal cleft, and supraumbilical raphe. We present four children with PHACE(S) syndrome who have absence of or severe malformation of the roots of their permanent first molars (PFMs). Root abnormalities in the children's molars were bilateral and not restricted to the segments affected by cutaneous hemangioma. The reason for root abnormalities is unknown, but given the rarity of these findings in healthy children, it is likely an additional dental manifestation of PHACE syndrome. The absence of functional roots in the PFMs can result in significant consequences. Therefore, we recommend a panoramic dental radiograph during transitional dentition for children with PHACE syndrome to screen for dental root abnormalities.