Sudden death due to nonarrhythmic cause in a patient with L-TGA.
Sudden death due to nonarrhythmic cause in a patient with L-TGA.
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L-TGA 患者因非心律失常原因突然死亡。
DOI：
10.1111/anec.12112
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发表时间：
2014
期刊：
影响因子：
--
通讯作者：
Tseng,ZianH
中科院分区：
文献类型：
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作者：
Hayward,RobertM;Ursell,PhilipC;Foster,Elyse;Tseng,ZianH
我们报告一例临床稳定的成人大动脉转位（l-TGA）猝死。据报道，猝死是l-TGA中的主要死亡原因，在没有其他可识别原因的情况下，通常归因于心律失常。然而，在这一人群中，非疾病原因对猝死负担的贡献尚不清楚。全面的尸检调查，包括尸检和起搏器询问，表明死亡原因是由于患者的机械三尖瓣（系统AV）狭窄导致的大量肺出血。这份报告强调了在这一人群中猝死的非药物原因的重要作用，以及尸检和器械询问在确定真正死因中的价值。
We report a case of sudden death in a clinically stable adult with l‐transposition of the great arteries (l‐TGA). Sudden death has been reported to be the leading cause of death in l‐TGA and is often attributed to arrhythmias in the absence of another identifiable cause. However, the contribution of nonarrhythmic causes to the burden of sudden death in this population is unknown. Comprehensive postmortem investigation, including autopsy and pacemaker interrogation, demonstrated that the cause of death was massive pulmonary hemorrhage due to stenosis of the patient's mechanical tricuspid (systemic AV) valve. This report highlights the important contribution of nonarrhythmic causes of sudden death in this population and the value of autopsy and device interrogation in determining true cause of death.