Congestive Myelopathy due to Intradural Spinal AVM Supplied by Artery of Adamkiewicz: Case Report with Brief Literature Review and Analysis of the Foix-Alajouanine Syndrome Definition.
Congestive Myelopathy due to Intradural Spinal AVM Supplied by Artery of Adamkiewicz: Case Report with Brief Literature Review and Analysis of the Foix-Alajouanine Syndrome Definition.
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DOI：
10.12659/pjr.894304
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发表时间：
2015
影响因子：
1.2
通讯作者：
Patel A
中科院分区：
文献类型：
--
作者：
Sood D;Mistry KA;Khatri GD;Chadha V;Garg S;Suthar PP;Patel DG;Patel A
脊髓动静脉畸形（AVM）可导致充血性脊髓病（Foix-Alajouanine综合征）的发展。脊髓动静脉畸形很少见，这种综合征也很少见。由于Foix-Alajouanine综合征的罕见性和混乱的定义，诊断经常被错过。我们报告一例47岁的男性患者患有这种罕见的综合征与AVM产生的动脉的Adamkiewicz，这是另一种罕见的。我们的患者通过使用20%胶栓塞病变进行治疗，之后他表现出症状轻度改善。我们还简要回顾了脊髓AVM的文献，并阐明了术语福克斯-阿拉乌宁综合征的演变。术语“Foix-Alajouanine综合征”的使用应限于因硬膜内脊髓AVM引起的充血性脊髓病而出现进行性亚急性至慢性神经系统症状的患者。CT血管造影应补充DSA作为初步成像方式。患者可以通过手术或血管内手术进行治疗。
Spinal arteriovenous malformations (AVMs) can lead to development of congestive myelopathy (Foix-Alajouanine syndrome). Spinal AVMs are rare and so is this syndrome. Diagnosis is often missed due to its rarity and confusing definitions of the Foix-Alajouanine syndrome. We report a case of a 47-year-old male patient suffering from this rare syndrome with an AVM arising from the artery of Adamkiewicz, which is another rarity. Our patient was treated by embolization of the lesion with 20% glue, after which he showed mild improvement of symptoms. We also present a brief review of literature on spinal AVMs and elucidate the evolution of the term Foix-Alajouanine syndrome. Use of the term “Foix-Alajouanine syndrome” should be restricted to patients with progressive subacute to chronic neurological symptoms due to congestive myelopathy caused by intradural spinal AVMs. CT angiography should supplement DSA as preliminary Imaging modality. Patients may be treated with surgery or endovascular procedures.