FIBROUS DYSPLASIA OF THE ORBIT
FIBROUS DYSPLASIA OF THE ORBIT
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DOI：
10.1136/bjo.78.4.266
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发表时间：
1994-04-01
影响因子：
4.1
通讯作者：
MCFADZEAN, R
中科院分区：
文献类型：
--
作者：
BIBBY, K;MCFADZEAN, R
本文回顾了12例眼眶纤维结构不良的病例，并描述了眼科表现。文中详细介绍了三个案例。6名患者接受了保守治疗；4名患者显示出疾病的放射进展。6名患者接受了手术。四名患者接受了保守手术，包括去除发育不良的骨骼--所有患者都需要进一步手术，包括两名患者的根治性切除。两名受试者接受了一次根治性手术。接受根治性手术的4例患者均未见复发。纤维异常增生症似乎不是一种仅限于青春期的疾病，而是可能会持续到成年，甚至中年。患者可能永远不需要手术，但需要对晚期进展进行随访。如果手术干预被认为是必要的，应该尝试切除所有发育不良的骨，因为保守手术后疾病的进展相对常见。
Twelve patients with fibrous dysplasia of the orbit are reviewed and the ophthalmic findings described. Three case histories are presented in detail. Six patients were managed conservatively; four have shown radiological progression of the disease. Six patients underwent surgery. A conservative procedure, comprising debulking dysplastic bone, was carried out in four - all required further surgery including radical excision in two patients. Two subjects had primary radical operations. No recurrence was encountered in the four patients who had undergone radical surgery. It would appear that fibrous dysplasia is not a disease confined to adolescence but may continue into adulthood, and even middle age. Patients may never require surgery, but require follow up for late progression. If surgical intervention is deemed necessary, an attempt should be made to excise all dysplastic bone, since progression of the disease after conservative surgery is relatively common.