Multicenter Study of Congenital Middle Ear Anomalies. Report on 246 Ears
Multicenter Study of Congenital Middle Ear Anomalies. Report on 246 Ears
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DOI：
10.1002/lary.29482
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发表时间：
2021-03-01
期刊：
影响因子：
2.6
通讯作者：
Imaizumi, Mitsuyoshi
中科院分区：
文献类型：
--
作者：
Ito, Tsukasa;Furukawa, Takatoshi;Imaizumi, Mitsuyoshi
目的/假设先天性中耳畸形是一种相对罕见的疾病。本研究旨在描述中耳畸形患者的特征和手术结果。方法对2008年1月至2017年12月期间接受初次手术治疗的先天性中耳畸形患者进行多中心研究。人口统计学、外科手术和听力测定数据登记到机构数据库中。结果246例患者（246耳），年龄4-75岁，中位年龄14岁。根据Teunissen和Cremers分类法对畸形进行了细分：I类53耳（22%），仅包括镫骨强直; II类35耳（14%），有听骨链畸形伴镫骨强直; III类139耳（57%），有听骨链畸形伴移动的镫骨-足板; Ⅳ级19耳（8%），伴卵圆窗发育不全。对198耳随访1年以上的听力结果进行评估，结果显示良好的术后ABG（
Objectives/Hypothesis Congenital middle ear anomalies represent a relatively rare condition. This study aimed to describe the characteristics and the surgical outcomes for patients with middle ear anomalies.Methods A multicenter study was conducted of consecutive patients with congenital middle ear anomalies who underwent primary surgical treatment between January 2008 and December 2017. Demographics, surgical procedures, and audiometric data were registered into the institutional database. Hearing changes and postoperative air-bone gap (ABG) were evaluated 1 year after surgery.Results A total of 246 patients (246 ears) (median age: 14 years, range: 4-75 years old) were included in this study. Anomalies were subdivided using the Teunissen and Cremers classification: 53 ears (22%) were categorized as class I, comprising only stapes ankylosis; 35 ears (14%) as class II, having ossicular chain anomalies with stapes ankylosis; 139 ears (57%) as class III, having ossicular chain anomalies with a mobile stapes-footplate; and 19 ears (8%) as class IV, with aplasia of the oval window. Evaluation of hearing outcomes for 198 ears with more than 1 year of follow-up revealed that good postoperative ABG (