Pneumatosis intestinalis in childhood dermatomyositis.
Pneumatosis intestinalis in childhood dermatomyositis.
复制标题
儿童皮肌炎中的肠积气症。
作者：
Miguel A. Oliveros;John J. Herbst;Patrick D. Lester;Fred A. Ziter
皮肌炎的胃肠道并发症是众所周知的。然而，文献回顾中未提及肠内肺病)。1-3虽然在进行性系统性硬化症中被注意到，但4-7其与皮肌炎的关联仅在一例中被记录，5在儿科文献中未被报道。将这种表面上良性的情况与继发于肠道穿孔的气腹区分开来是很重要的，后者是皮肌炎的严重并发症
The gastrointestinal complications of dermatomyositis are well known. Reviews, however, do not mention pneumatosis intestinalis in this disorder).1-3 Although noted in progressive systemic sclerosis,4-7 its association with dermatomyositis has been documented in only one case,5 unreported in the pediatric literature. It is important to distinguish this apparently benign condition from pneumoperitoneum secondary to intestinal perforation, which is a grave complication of dermatomyositis.1
CASE REPORT
W. W., an 8-8/12-year-old girl with a three-year history of dermatomyositis with prominent skin rash, disseminated subcutaneous calcification, muscle wasting and induration, also complained of occasional abdominal pain, recently localized to the right hypochondriurn and right shoulder. Inspite of continuous prednisone treatment and intermittent trials of azathioprine, methotrexate, and cyclophosphamide the patient's disease failed to remit.