BEHCETS SYNDROME IN A FAMILY WITH INFLAMMATORY BOWEL-DISEASE
BEHCETS SYNDROME IN A FAMILY WITH INFLAMMATORY BOWEL-DISEASE
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DOI：
10.1001/archinte.145.6.1047
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发表时间：
1985-01-01
影响因子：
--
通讯作者：
WHITE, RH
中科院分区：
文献类型：
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作者：
YIM, CW;WHITE, RH
虽然白塞综合征和炎症性肠病的胃肠道和全身特征在相当大程度上重叠，但它们通常被视为2种不同的疾病。对一个患有炎症性肠病的家庭的三名成员进行了评估，其中2人符合白塞综合征的标准。先证者具有克罗恩氏回肠结肠炎和白塞氏综合征的典型特征。一个从未符合白塞综合征标准的女儿因溃疡性结肠炎接受了结肠切除术。第二个女儿具有典型的白塞综合征特征，包括结肠炎反复发作伴结肠明显阿弗他溃疡。炎症性肠病和白塞综合征可能密切相关，是疾病谱的一部分，而不是不同的疾病实体。
Although the gastrointestinal and systemic features of Behcet''s syndrome and inflammatory bowel disease overlap to a considerable extent, they are generally viewed as 2 distinct diseases. Three members of a family who had inflammatory bowel lesions, 2 of whom met criteria for Behcet''s syndrome, were evaluated. The propositus had classic features of both Crohn''s ileocolitis and Behcet''s syndrome. A daughter, who never met criteria for Behcet''s syndrome, had undergone colectomy for ulcerative colitis. A 2nd daughter had classic features of Behcet''s syndrome, including recurrent episodes of colitis with distinct aphthous ulcers in the colon. Inflammatory bowel disease and Behcet''s syndrome may be closely related and part of a spectrum of disease rather than distinct disease entities.