Evaluation of the lumbar spine in patients with glycogen storage disease: CT demonstration of patterns of paraspinal muscle atrophy.
Evaluation of the lumbar spine in patients with glycogen storage disease: CT demonstration of patterns of paraspinal muscle atrophy.
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糖原累积病患者腰椎的评估：椎旁肌萎缩模式的 CT 演示。
DOI：
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发表时间：
1991
期刊：
影响因子：
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通讯作者：
R. Hyman
中科院分区：
文献类型：
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作者：
J. Cinnamon;A. Slonim;K. Black;M. T. Gorey;Donna Maria Scuderi;R. Hyman
对 19 名糖原累积病患者进行了腰椎 CT 研究。 10 名麦卡德尔病患者中的 9 名和 9 名酸性麦芽糖酶缺乏症患者中的 7 名表现出与年龄不成比例的后椎旁肌萎缩。此外，所有 10 名麦卡德尔病患者的腰肌均未受影响，而 9 名酸性麦芽糖酶缺乏症患者中的 7 名出现萎缩。我们的结论是，当腰痛患者或无症状患者表现出无法解释的椎旁肌肉萎缩时，应考虑糖原累积病的诊断。此外，当腰肌不受累时，建议对麦卡德尔病进行具体诊断。
CT studies of the lumbar spine were performed in 19 patients with glycogen storage disease. Nine of 10 patients with McArdle's disease and seven of nine patients with acid maltase deficiency demonstrated posterior paraspinal muscle atrophy out of proportion to their ages. In addition, the psoas muscles were spared in all 10 patients with McArdle's disease and were involved with atrophy in seven of the nine patients with acid maltase deficiency. We conclude that when patients with low back pain-or asymptomatic patients-demonstrate otherwise unexplained atrophy of the paraspinal muscles the diagnosis of glycogen storage disease should be considered. Furthermore, when the psoas muscles are spared, the specific diagnosis of McArdle's disease is suggested.