Systemic lupus erythematosus associated with moyamoya syndrome
Systemic lupus erythematosus associated with moyamoya syndrome
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DOI：
10.1191/096120300678828686
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发表时间：
2000-01-01
期刊：
影响因子：
2.6
通讯作者：
Al Rayes, HM
中科院分区：
文献类型：
--
作者：
El Ramahi, KM;Al Rayes, HM
烟雾病是一种罕见的临床实体，其特征是双侧颈内动脉闭塞和侧支动脉的发展。一名18岁的沙特男性系统性红斑狼疮（SLE）表现为轻度右侧轻偏瘫，随后复发性缺血性卒中。脑血管造影显示双侧颈内动脉狭窄与侧支循环（烟雾血管）的发展。没有证据表明活动性SLE或其他脑闭塞的危险因素，如抗磷脂抗体综合征;药物和手术干预不影响复发性缺血性损伤的不良结局。
Moyamoya disease is an uncommon clinical entity, characterized by bilateral occlusion of the internal carotid artery and the development of collateral arteries. An 18-year-old Saudi male with systemic lupus erythematosus (SLE) presented with mild right hemiparesis, followed by recurrent ischemic stroke. Cerebral angiography showed bilateral internal carotid artery stenosis associated with the development of collateral circulation (moyamoya vessels). There was no evidence of active SLE or other risk factors for cerebral occlusion, such as antiphospholipid antibody syndrome; Medical and surgical interventions did not influence the poor outcome of the recur-rent ischemic insults.