Retinal vein occlusion in retinal racemose hemangioma: a case report and literature review of ocular complications in this rare retinal vascular disorder
Retinal vein occlusion in retinal racemose hemangioma: a case report and literature review of ocular complications in this rare retinal vascular disorder
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DOI：
10.1186/1471-2415-14-101
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发表时间：
2014-08-21
影响因子：
2
通讯作者：
Lai, Kun
中科院分区：
文献类型：
--
作者：
Qin, Xue-jiao;Huang, Chao;Lai, Kun
背景：视网膜总状血管瘤(RRH)是一种罕见的先天性疾病，常与其他眼部并发症并存。在本研究中，我们报告一例RRH合并三支视网膜静脉阻塞的病例，并就眼部并发症及其与RRH的关系作一综述。患者的眼底检查、荧光素血管造影(FFA)和光学相干断层扫描(OCT)证实，第3组RRH合并视网膜静脉阻塞，位于颞上、颞下和鼻下分支。检测到导致视力障碍的黄斑水肿。文中还对相关文献进行了简要回顾。在PubMed数据库中搜索RRH或相关关键词，以查找2013年12月31日或之前发表的关于眼部并发症或相关性的报告。总共发现了140篇文章，描述167例RRH病例。平均确诊年龄为22.97岁。眼部并发症32例(19.16%)。视网膜静脉阻塞(46.88%)是RRH的主要眼部并发症，其次是出血(34.38%)。8例(4.79%)合并其他眼部疾病，如Sturge-Weber综合征、晨光盘畸形、大动脉瘤等。结论：虽然RRH是一种相对非进展性的疾病，但其并发症可能导致视力丧失，应及时治疗。
Backgroud: Retinal racemose hemangioma (RRH) is a rare congenital disorder that often co-occurs with other ocular complications. In this study, we present a case of RRH complicated with retinal vein obstruction in three branches and provide a review of ocular complications and associations with RRH.Case presentation: One case of RRH is presented. Fundus examination, fluorescein angiography (FFA) and optical coherence tomography (OCT) of the patient identified Group 3 RRH complicated with retinal vein occlusions in the superotemporal, inferotemporal, and inferonasal branches. Macular edema, which causes visual impairment, was detected. A brief literature review was also presented. The PubMed database was searched for RRH or related keywords to find reports of ocular complications or associations published on or before Dec. 31, 2013. A total of 140 papers describing167 RRH cases were found. The mean age of diagnosis was 22.97 years. Ocular complications were mentioned in 32 (19.16%) cases. Retinal vein occlusion (46.88%) was the major ocular complication in RRH, followed by hemorrhage (34.38%). Eight (4.79%) cases were associated with other ocular diseases such as Sturge-Weber syndrome, Morning glory disc anomaly and macroaneurysm.Conclusions: Although RRH is a relatively non-progressive condition, its complications may lead to vision loss and should be treated in time.