Endovascular treatment of a carotid dissecting pseudoaneurysm in a patient with Ehlers-Danlos syndrome type IV with fatal outcome
Endovascular treatment of a carotid dissecting pseudoaneurysm in a patient with Ehlers-Danlos syndrome type IV with fatal outcome
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DOI：
10.1007/s00270-007-9135-1
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发表时间：
2008-01-01
影响因子：
2.9
通讯作者：
Duddy, Martin J.
中科院分区：
文献类型：
--
作者：
Lim, Siok Ping;Duddy, Martin J.
我们报告一位患有Ehlers-Danlos综合征IV型（EDS IV）的患者，其颈动脉夹层假性动脉瘤导致严重的颈动脉狭窄。对该病变进行了血管内治疗。不幸的是，患者死于远端血管灾难（颅内出血和腹主动脉破裂）。这一独特病例说明了EDS IV患者血管内治疗的风险以及术前筛查伴随病变的必要性。它还表明，夹层假性动脉瘤可以用覆膜支架治疗，并且在EDS IV患者中使用Angioseal闭合是有效的。
We present a patient with Ehlers-Danlos syndrome type IV (EDS IV) with a carotid dissecting pseudoaneurysm causing severe carotid stenosis. This lesion was treated endovascularly. Unfortunately, the patient died of remote vascular catastrophes (intracranial hemorrhage and abdominal aortic rupture). This unique case illustrates the perils of endovascular treatment of EDS IV patients and the need for preoperative screening for concomitant lesions. It also shows that a dissecting pseudoaneurysm can feasibly be treated with a covered stent and that closure is effective using Angioseal in patients with EDS IV.