Multifocal meningioangiomatosis in a 3-year-old patient.
Multifocal meningioangiomatosis in a 3-year-old patient.
复制标题
一名3岁患者的多灶性脑膜血管瘤病。
DOI：
10.3171/2012.9.peds1224
复制
发表时间：
2012-12
期刊：
影响因子：
--
通讯作者：
Smith E
中科院分区：
文献类型：
--
作者：
Jamil O;Ramkissoon S;Folkerth R;Smith E
脑膜血管瘤病由脑和软脑膜的良性错构瘤性病变组成，通常表现为癫痫发作。管理是基于切除和药物控制癫痫发作。病变通常是孤立的。多发性脑膜血管瘤病是非常罕见的，只有2例报告在成人和儿童。作者报告了第一例，据他们所知，多灶性脑膜血管瘤病的儿童。这个独特的病例突出了与这些病变相关的治疗挑战，并证明了多灶性在儿科人群中是可能的。这一发现对患有这些肿瘤的儿童的诊断和随访具有重要意义。
Meningioangiomatosis consists of benign hamartomatous lesions of the brain and the leptomeninges, which typically present with seizure. Management is predicated on resection and control of seizures with medication. Lesions are typically solitary. Multifocal meningioangiomatosis is extremely rare, with only 2 cases reported in adults and none in children. The authors report the first case, to their knowledge, of multifocal meningioangiomatosis in a child. This unique case highlights therapeutic challenges associated with these lesions and demonstrates that multifocality is possible in the pediatric population. This finding has implications for diagnosis and follow-up for children afflicted with these tumors.